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BL1S3 rabbit pAb

商品貨號： PLA020629

適應(yīng) 性： 人,小鼠

￥600元

規(guī)格：

40μL 100μL 200μL

在線咨詢

MSDS

說明書

商品描述

基因名稱： BLOC1S3 BLOS3
蛋白名稱： BL1S3
Human_gene_id： 388552
Human_gene_link： http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=388552
Human_swiss_prot_no： Q6QNY0
Human_swiss_link： https://www.uniprot.org/uniprotkb/Q6QNY0/entry
Mouse_gene_id： 232946
Mouse_gene_link： https://www.uniprot.org/uniprot/232946
Mouse_swiss_prot_no： Q5U5M8
Mouse_swiss_link： https://www.uniprot.org/uniprotkb/Q5U5M8
特異性： This antibody detects endogenous levels of BL1S3 at Human/Mouse
組成： Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
來源： Polyclonal, Rabbit,IgG
稀釋： WB 1：500-2000
純化工藝： The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
濃度： 1 mg/ml
儲存： -15°C to -25°C/1 year(Do not lower than -25°C)
說明書： 1
Msds： MSDS_Antibody.pdf
分子量： 22kD
功能： disease:Defects in BLOC1S3 are the cause of Hermansky-Pudlak syndrome type 8 (HPS8) [MIM:203300]. Hermansky-Pudlak syndrome (HPS) is a genetically heterogeneous, rare, autosomal recessive disorder characterized by oculocutaneous albinism, bleeding due to platelet storage pool deficiency, and lysosomal storage defects. This syndrome results from defects of diverse cytoplasmic organelles including melanosomes, platelet dense granules and lysosomes. Ceroid storage in the lungs is associated with pulmonary fibrosis, a common cause of premature death in individuals with HPS.,function:May play a role in the biogenesis of melanosomes and other specialized organelles of the endosomal-lysosomal system.,PTM:Phosphorylated.,similarity:Belongs to the BLOC1S3 family.,subunit:Component of the biogenesis of lysosome-related organelles (BLOC-1) complex which is composed of BLOC1S1, BLOC1S2, DTNBP1, MUTED, PLDN, CNO/cappuccino and SNAPAP. Interacts directly with BLOC1S2.,
相關(guān)產(chǎn)品： RS0001,RS0002,YM3028,YM3029
細胞定位： Cytoplasm .
科研貨號： PLA020629

BL1S3 rabbit pAb

Catalog No PLA020629

Product information

基因名稱： BLOC1S3 BLOS3
蛋白名稱： BL1S3
Human_gene_id： 388552
Human_gene_link： http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=388552
Human_swiss_prot_no： Q6QNY0
Human_swiss_link： https://www.uniprot.org/uniprotkb/Q6QNY0/entry
Mouse_gene_id： 232946
Mouse_gene_link： https://www.uniprot.org/uniprot/232946
Mouse_swiss_prot_no： Q5U5M8
Mouse_swiss_link： https://www.uniprot.org/uniprotkb/Q5U5M8
特異性： This antibody detects endogenous levels of BL1S3 at Human/Mouse
組成： Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
來源： Polyclonal, Rabbit,IgG
稀釋： WB 1：500-2000
純化工藝： The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
濃度： 1 mg/ml
儲存： -15°C to -25°C/1 year(Do not lower than -25°C)
說明書： 1
Msds： MSDS_Antibody.pdf
分子量： 22kD
功能： disease:Defects in BLOC1S3 are the cause of Hermansky-Pudlak syndrome type 8 (HPS8) [MIM:203300]. Hermansky-Pudlak syndrome (HPS) is a genetically heterogeneous, rare, autosomal recessive disorder characterized by oculocutaneous albinism, bleeding due to platelet storage pool deficiency, and lysosomal storage defects. This syndrome results from defects of diverse cytoplasmic organelles including melanosomes, platelet dense granules and lysosomes. Ceroid storage in the lungs is associated with pulmonary fibrosis, a common cause of premature death in individuals with HPS.,function:May play a role in the biogenesis of melanosomes and other specialized organelles of the endosomal-lysosomal system.,PTM:Phosphorylated.,similarity:Belongs to the BLOC1S3 family.,subunit:Component of the biogenesis of lysosome-related organelles (BLOC-1) complex which is composed of BLOC1S1, BLOC1S2, DTNBP1, MUTED, PLDN, CNO/cappuccino and SNAPAP. Interacts directly with BLOC1S2.,
相關(guān)產(chǎn)品： RS0001,RS0002,YM3028,YM3029
細胞定位： Cytoplasm .
科研貨號： PLA020629

Hunan UPT Biotechnology Co.,Ltd

Website：m.tjdqdt.com Servive hotline :4006916686

E-mail：service@uptbio.com

Address：

Room 402, Building 13, Xinggong International Industrial Park, 100 Guyuan Road, Yuelu District, Changsha City, Hunan Province, China.

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